Human (129 sources):
Abnormal brain FDG positron emission tomography,
Abnormal cerebellum morphology,
Abnormal cerebral white matter morphology,
Abnormal lower motor neuron morphology,
Abnormal mitochondrial morphology,
Abnormal pyramidal sign,
Abnormal respiratory system physiology,
Abnormal upper motor neuron morphology,
Abnormality of extrapyramidal motor function,
Absent Achilles reflex,
Abulia,
Aggressive behavior,
Agitation,
Amyotrophic lateral sclerosis,
Anxiety,
Apathy,
Apraxia,
Astrocytosis,
Babinski sign,
Behavioral abnormality,
Bilateral sensorineural hearing impairment,
Bilateral tonic-clonic seizure,
Bone pain,
Bulbar palsy,
Cerebellar atrophy,
Cerebral cortical atrophy,
Clumsiness,
Cognitive impairment,
Collectionism,
Degeneration of anterior horn cells,
Degeneration of the lateral corticospinal tracts,
Depression,
Difficulty walking,
Disinhibition,
Distal amyotrophy,
Distal muscle weakness,
Distal upper limb amyotrophy,
Distal upper limb muscle weakness,
Dysarthria,
Dyscalculia,
Dysdiadochokinesis,
Dysgraphia,
Dyslexia,
Dysmetria,
Dysphagia,
Dysphasia,
Dyspnea,
Dystonia,
EEG with continuous slow activity,
EMG: myopathic abnormalities,
Echolalia,
Elevated circulating alkaline phosphatase concentration,
Elevated circulating creatine kinase concentration,
Emotional blunting,
Emotional lability,
Facial palsy,
Fasciculations,
Fatigable weakness of bulbar muscles,
Fatigable weakness of respiratory muscles,
Fatigable weakness of swallowing muscles,
Fatigue,
Foot dorsiflexor weakness,
Fractures of the long bones,
Frontotemporal cerebral atrophy,
Frontotemporal dementia,
Gait ataxia,
Gait disturbance,
Generalized amyotrophy,
Generalized muscle weakness,
Gliosis,
Global brain atrophy,
Hallucinations,
Hearing impairment,
Hyperorality,
Hyperreflexia,
Hyporeflexia,
Inappropriate behavior,
Intrinsic hand muscle atrophy,
Irritability,
Lack of insight,
Language impairment,
Laryngospasm,
Limb ataxia,
Loss of speech,
Memory impairment,
Mental deterioration,
Mildly elevated creatine kinase,
Motor stereotypy,
Muscle spasm,
Muscle weakness,
Mutism,
Myopathy,
Nausea and vomiting,
Neurodegeneration,
Neuronal loss in the cerebral cortex,
Nystagmus,
Oculomotor apraxia,
Osteolysis,
Osteosarcoma,
Pain,
Paralysis,
Paraparesis,
Parkinsonism,
Patchy osteosclerosis,
Perseveration,
Personality changes,
Poor speech,
Progressive cerebellar ataxia,
Proximal muscle weakness,
Psychosis,
Ptosis,
Respiratory insufficiency,
Restlessness,
Restrictive behavior,
Rimmed vacuoles,
Scapular winging,
Skeletal muscle atrophy,
Spasticity,
Steppage gait,
Supranuclear gaze palsy,
Tetraparesis,
Thickened nuchal skin fold,
Tremor,
Upper motor neuron dysfunction,
Urinary incontinence,
Vertical supranuclear gaze palsy,
Weakness due to upper motor neuron dysfunction,
Weakness of long finger extensor muscles,
Xerostomia
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