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Summary Expression Phenotypes Gene Literature (1) GO Terms (44) Nucleotides (115) Proteins (41) Interactants (141) Wiki
XB-GENEPAGE-1013274
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 lonp1

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lon peptidase 1, mitochondrial

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( Nomenclature history )

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Mitochondrial ATP-dependent protease PIM1/LON

Protein Function :
ATP-dependent serine protease that mediates the selective degradation of misfolded, unassembled or oxidatively damaged polypeptides as well as certain short-lived regulatory proteins in the mitochondri...[+]


InterPro :
ATPase AAA core, Peptidase S16 AS, Ribosomal S5 D2-typ fold, PUA-like sf, [+]

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Diseases: 


Disease Ontology:
CODAS syndrome

MIM:
CODAS SYNDROME

External Links:
 
???displayGene.expression???                  Development Stages                                               Embryonic Tissues                                                                Adult Tissues
More Information
Xenbase Expression Details In situ images Single cell data at SPRING In situ: RNA-Seq:


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