The etfbkmt gene encodes a methyltransferase protein localized to the mitochondrial matrix. This enzyme catalyzes the trimethylation of a specific lysine residue on the electron transfer flavoprotein a...[+]

The etfbkmt gene encodes a methyltransferase protein localized to the mitochondrial matrix. This enzyme catalyzes the trimethylation of a specific lysine residue on the electron transfer flavoprotein alpha subunit (etfa), a key post-translational modification required for its proper function within the mitochondrial beta-oxidation pathway. Expression is detected in the brain and eye during development. [-]

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