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Summary Expression Phenotypes Gene Literature (1) GO Terms (9) Nucleotides (115) Proteins (41) Interactants (142) Wiki
XB-GENEPAGE-1013274
Gene Symbol:
 lonp1

Gene Name: 
lon peptidase 1, mitochondrial

Synonyms:
( Nomenclature history )

Gene Function:
Mitochondrial ATP-dependent protease PIM1/LON

Protein Function :
ATP-dependent serine protease that mediates the selective degradation of misfolded, unassembled or oxidatively damaged polypeptides as well as certain short-lived regulatory proteins in the mitochondri...[+]


InterPro :
ATPase AAA core, Peptidase S16 AS, Ribosomal S5 D2-typ fold, PUA-like sf, [+]

Interactants:
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Diseases: 


Disease Ontology:
CODAS syndrome

OMIM:
CODAS SYNDROME

External Links:
 
Expression                  Development Stages                                               Embryonic Tissues                                                                Adult Tissues
More Information
Xenbase Expression Details In situ images Single cell data at SPRING In situ: RNA-Seq:


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